Modern management of severe platelet function disorders

Jayanthi Alamelu; Ri Liesner

doi:10.1111/j.1365-2141.2010.08191.x

Modern management of severe platelet function disorders

Jayanthi Alamelu^*, Ri Liesner

^*Corresponding author for this work

Great Ormond St Hosp Sick Children, University College London, University of London

Research output: Contribution to journal › Literature review › peer-review

72 Citations (Scopus)

Abstract

Severe platelet function defects are rare disorders that require expertise in diagnosis and management. Therefore patients with such disorders should be referred to and managed in centres with the full laboratory repertoire of tests and clinical support necessary to optimise their quality of care. The aim of this review is to discuss the management of these patients in various clinical situations including surgical intervention.

Original language	English
Pages (from-to)	813-823
Number of pages	11
Journal	British Journal of Haematology
Volume	149
Issue number	6
DOIs	https://doi.org/10.1111/j.1365-2141.2010.08191.x
Publication status	Published - Jun 2010

Keywords

platelet function disorders
Glanzmann Thrombasthenia
Bernard-Soulier Syndrome
BERNARD-SOULIER-SYNDROME
RECOMBINANT FACTOR-VIIA
BONE-MARROW-TRANSPLANTATION
STEM-CELL TRANSPLANTATION
GLYCOPROTEIN-IB-ALPHA
OF-THE-LITERATURE
HERMANSKY-PUDLAK-SYNDROME
STORAGE-POOL-DISEASE
GLANZMANNS-THROMBASTHENIA
BLEEDING DISORDERS

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title = "Modern management of severe platelet function disorders",

abstract = "Severe platelet function defects are rare disorders that require expertise in diagnosis and management. Therefore patients with such disorders should be referred to and managed in centres with the full laboratory repertoire of tests and clinical support necessary to optimise their quality of care. The aim of this review is to discuss the management of these patients in various clinical situations including surgical intervention.",

keywords = "platelet function disorders, Glanzmann Thrombasthenia, Bernard-Soulier Syndrome, BERNARD-SOULIER-SYNDROME, RECOMBINANT FACTOR-VIIA, BONE-MARROW-TRANSPLANTATION, STEM-CELL TRANSPLANTATION, GLYCOPROTEIN-IB-ALPHA, OF-THE-LITERATURE, HERMANSKY-PUDLAK-SYNDROME, STORAGE-POOL-DISEASE, GLANZMANNS-THROMBASTHENIA, BLEEDING DISORDERS",

author = "Jayanthi Alamelu and Ri Liesner",

year = "2010",

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doi = "10.1111/j.1365-2141.2010.08191.x",

language = "English",

volume = "149",

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TY - JOUR

T1 - Modern management of severe platelet function disorders

AU - Alamelu, Jayanthi

AU - Liesner, Ri

PY - 2010/6

Y1 - 2010/6

N2 - Severe platelet function defects are rare disorders that require expertise in diagnosis and management. Therefore patients with such disorders should be referred to and managed in centres with the full laboratory repertoire of tests and clinical support necessary to optimise their quality of care. The aim of this review is to discuss the management of these patients in various clinical situations including surgical intervention.

AB - Severe platelet function defects are rare disorders that require expertise in diagnosis and management. Therefore patients with such disorders should be referred to and managed in centres with the full laboratory repertoire of tests and clinical support necessary to optimise their quality of care. The aim of this review is to discuss the management of these patients in various clinical situations including surgical intervention.

KW - platelet function disorders

KW - Glanzmann Thrombasthenia

KW - Bernard-Soulier Syndrome

KW - BERNARD-SOULIER-SYNDROME

KW - RECOMBINANT FACTOR-VIIA

KW - BONE-MARROW-TRANSPLANTATION

KW - STEM-CELL TRANSPLANTATION

KW - GLYCOPROTEIN-IB-ALPHA

KW - OF-THE-LITERATURE

KW - HERMANSKY-PUDLAK-SYNDROME

KW - STORAGE-POOL-DISEASE

KW - GLANZMANNS-THROMBASTHENIA

KW - BLEEDING DISORDERS

U2 - 10.1111/j.1365-2141.2010.08191.x

DO - 10.1111/j.1365-2141.2010.08191.x

M3 - Literature review

SN - 0007-1048

VL - 149

SP - 813

EP - 823

JO - British Journal of Haematology

JF - British Journal of Haematology

IS - 6

ER -

Modern management of severe platelet function disorders

Abstract

Keywords

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